Overview
- SupplierGeneTex
- Product NameACADVL antibody [N1C1]
- Delivery Days Customer9
- CertificationResearch Use Only
- Concentration0.3 mg/ml
- IsotypeIgG
- Scientific DescriptionThe protein encoded by this gene is targeted to the inner mitochondrial membrane where it catalyzes the first step of the mitochondrial fatty acid beta-oxidation pathway. This acyl-Coenzyme A dehydrogenase is specific to long-chain and very-long-chain fatty acids. A deficiency in this gene product reduces myocardial fatty acid beta-oxidation and is associated with cardiomyopathy. Alternative splicing results in multiple transcript variants encoding different isoforms. [provided by RefSeq]
- Storage Instruction2°C to 8°C,-20°C
- UNSPSC12352203
References
- Mitochondrial morphology, bioenergetics and proteomic responses in fatty acid oxidation disorders. Raimo S et al., 2021 May, Redox BiolRead more
- Mitoregulin: A lncRNA-Encoded Microprotein that Supports Mitochondrial Supercomplexes and Respiratory Efficiency. Stein CS et al., 2018 Jun 26, Cell RepRead more
- NAD+ Repletion Reverses Heart Failure With Preserved Ejection Fraction. Tong D et al., 2021 May 28, Circ ResRead more
- Nitric oxide regulates mitochondrial fatty acid metabolism through reversible protein S-nitrosylation. Doulias PT et al., 2013 Jan 1, Sci SignalRead more
- Oral nitrite restores age-dependent phenotypes in eNOS-null mice. Tenopoulou M et al., 2018 Aug 23, JCI InsightRead more
- Quantitative proteomics identifies FOLR1 to drive sorafenib resistance via activating autophagy in hepatocellular carcinoma cells. Chu H et al., 2021 May 28, CarcinogenesisRead more
- Strategies for correcting very long chain acyl-CoA dehydrogenase deficiency. Tenopoulou M et al., 2015 Apr 17, J Biol ChemRead more