ASL antibody - Orthogonal Validated

Catalog number: GTX113629_100ul
Brand: GeneTex
Packing: 100 ul
Other sizes: 25 ul
Price: € 334.00
Expected delivery time: 10 days
Quantity:
GTX113629 ICC/IF Image
GTX113629 ICC/IF Image...
GTX113629 WB Image
GTX113629 IHC-P Image...
GTX113629 ICC/IF Image
GTX113629 IHC-P Image...
GTX113629 IHC-P Image
GTX113629 WB Image...
GTX113629 IHC-P Image
GTX113629 WB Image...
GTX113629 WB Image
GTX113629 ICC/IF Image...

Product specifications for - ASL antibody - Orthogonal Validated

Overview: 
Product group: Antibodies
Category: Primary Antibodies
Application: ImmunoCytoChemistry; ImmunoFluorescence; ImmunoHistoChemistry; ImmunoHistoChemistry Parrafin; Western Blot
Species: Human, Mouse
Host: Rabbit
Target: ASL
Target description: argininosuccinate lyase
Clonality: Polyclonal
Conjugation: Unconjugated
Isotype: IgG
Properties: 
Datasheet: Datasheet
  Research Use Only
UNSPSC: 12352203
Concentration: 0.44 mg/ml
Storage instructions: 2-¦C to 8-¦C, -20-¦C or -80-¦C
Scientific information: 
Scientific info: This gene encodes a member of the lyase 1 family. The encoded protein forms a cytosolic homotetramer and primarily catalyzes the reversible hydrolytic cleavage of argininosuccinate into arginine and fumarate, an essential step in the liver in detoxifying ammonia via the urea cycle. Mutations in this gene result in the autosomal recessive disorder argininosuccinic aciduria, or argininosuccinic acid lyase deficiency. A nontranscribed pseudogene is also located on the long arm of chromosome 22. Alternatively spliced transcript variants encoding different isoforms have been described. [provided by RefSeq]
Gene ID: 435
Swiss prot ID: P04424
Additional information: 
Synonyms: argininosuccinase; argininosuccinate lyase; arginosuccinase; ASAL
Understanding the role of argininosuccinate lyase transcript variants in the clinical and biochemical variability of the urea cycle disorder argininosuccinic aciduria. Hu L et al., 2013 Nov 29, J Biol Chem Read more
Understanding the role of argininosuccinate lyase transcript variants in the clinical and biochemical variability of the urea cycle disorder argininosuccinic aciduria. Hu L et al., 2013 Nov 29, J Biol Chem Read more